Publication:

An unusual variant of Klippel-Trenaunay syndrome

A twenty four year old male presented with complaints of pain and recurrent non healing ulcer over the medial aspect of the right leg. He had dilated and tortuous veins with mild hypertrophy of the right lower limb. Ultrasound and ascending lower limb venogram revealed absence of common femoral, superficial femoral and iliac veins on the right side. The popliteal vein was seen to continue as a medial venous channel, crossing in the pelvis to the left side and draining into the left common femoral vein. Klippel-Trenaunay syndrome with dilated medial venous channel draining into the opposite common femoral vein have so far not been described in the literature to our knowledge. This case is presented for its rarity.A twenty four year old male presented with complaints of pain and recurrent non healing ulcer over the medial aspect of the right leg. He had dilated and tortuous veins with mild hypertrophy of the right lower limb. Ultrasound and ascending lower limb venogram revealed absence of common femoral, superficial femoral and iliac veins on the right side. The popliteal vein was seen to continue as a medial venous channel, crossing in the pelvis to the left side and draining into the left common femoral vein. Klippel-Trenaunay syndrome with dilated medial venous channel draining into the opposite common femoral vein have so far not been described in the literature to our knowledge. This case is presented for its rarity. Keywords: Varicose veins, Venogram, Ultrasound, Klippel-Trenaunay syndrome