Publication:

A case report on uterus didelphys with unilateral renal agenesis and crouzon syndrome

Uterus didelphys is a type of Müllerian duct anomaly where there is complete duplication of uterine horns and the cervix, with no communication between them, which can be associated with abnormalities of the renal system as seen in this case of a 17 year girl, who attained menarche at 13 years of age and had regular cycles presented with dysmenorrhea. Examination and imaging showed right ovarian cystic mass. Incidentally left unilateral solitary kidney was found. Physical examination showed features of Crouzon Syndrome which is an autosomal dominant genetic disorder also known as Branchial Arch Syndrome. She was admitted for treatment of the symptomatic right adnexal mass. Laparotomy was done. Findings were, a dense adherent mass of 6 × 6 cm in right iliac fossa, uterus didelphys with left uterine horn, normal left fallopian tube and ovary, right side hematosalphinx adherent to enlarged right uterine horn of 10 weeks size and right side chocolate cyst.  Appendix was elongated with faecolith. Adhesiolysis with removal of right non communicating horn with fallopian tube and ovary and appendicectomy was done.